openalexFrontiers in Gastroenterology2026-07-24
Congenital hepatic fibrosis in an adult female combined with Von Meyenburg complex and autosomal dominant polycystic kidney disease: a case report
Xinrui Ren, Yu Cui, Jiayi Song, Yiwen Tang, X C Xie, Wanchun Zhu, et al.
Background Congenital hepatic fibrosis (CHF) is a rare disease associated with the polycystic kidney gene, and the initial symptoms are often associated with portal hypertension, such as splenomegaly and esophageal varices. While the basic clinical features and pathogenesis of is…